Authors of section

Authors

Scott Bartlett, Michael Ehrenfeld, Gerson Mast, Adrian Sugar

Executive Editor

Edward Ellis III

General Editor

Daniel Buchbinder

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Intraorbital hypertelorism with midface defect

Orbital hypertelorism is not a syndrome, but a physical finding in many craniofacial anomalies. It is defined as an increase in the bony interorbital distance. The ethmoid sinuses are normally over-expanded and in some cases of severe hypertelorism, there is an inferior displacement of the cribriform plate.

The midface is in some cases affected with an inverted V-shaped occlusal plane in the maxilla.

definition

Etiology
It is both etiologically and pathogenetically heterogenous and can be found in patients with:

  • Frontonasal Malformation
  • Craniofrontonasal Dysplasia
  • Median and Paramedian Craniofacial Clefts
  • Craniosynostosis